{"id":56867,"date":"2022-12-09T13:16:49","date_gmt":"2022-12-09T12:16:49","guid":{"rendered":"https:\/\/www.fiftyandmemagazine.be\/fr\/?p=56867"},"modified":"2022-12-09T13:16:49","modified_gmt":"2022-12-09T12:16:49","slug":"celine-dion-en-quoi-consiste-sa-maladie","status":"publish","type":"post","link":"https:\/\/www.fiftyandmemagazine.be\/fr\/sante\/celine-dion-en-quoi-consiste-sa-maladie","title":{"rendered":"C\u00e9line Dion : en quoi consiste sa maladie ?"},"content":{"rendered":"<span class=\"span-reading-time rt-reading-time\" style=\"display: block;\"><span class=\"rt-label rt-prefix\">Reading Time: <\/span> <span class=\"rt-time\"> 2<\/span> <span class=\"rt-label rt-postfix\">minutes<\/span><\/span><p>Les fans de <strong>C\u00e9line Dion<\/strong> ont appris le report en 2024 de plusieurs dates europ\u00e9ennes de la tourn\u00e9e &lsquo;Courage World Tour 2023&rsquo;. La chanteuse canadienne a annonc\u00e9 sur son compte Instagram souffrir des sympt\u00f4mes du syndrome de la personne raide (SPR). Une maladie neurologique qui m\u00e9rite que l\u2019on s\u2019y attarde. Pour sa raret\u00e9 et sa cible : des femmes, pour la majorit\u00e9 des cas, avec un pic d\u2019incidence situ\u00e9 autour des 45 ans.<\/p>\n<h2>Le SPR dont souffre C\u00e9line Dion en bref<\/h2>\n<p>Peu connu du grand public, le syndrome de la personne raide, appel\u00e9 aussi syndrome de Moersch-Woltman, constitue une maladie neurologique rare. La pr\u00e9valence est estim\u00e9e \u00e0 une personne sur un million. La maladie toucherait deux fois plus les femmes que les hommes. Quant au profil type du malade concern\u00e9, il concerne plus fr\u00e9quemment des personnes atteintes par le diab\u00e8te de type 1, certaines maladies auto-immunes ou des cancers. Dont celui du sein, du poumon, de la thyro\u00efde ou du c\u00f4lon. Une maladie encore entour\u00e9e de certaines zones d\u2019ombre. Comme certaines causes encore inconnues et \u00e0 l\u2019origine du d\u00e9clenchement des sympt\u00f4mes.<\/p>\n<h2>\nDes sympt\u00f4mes s\u00e9v\u00e8res<\/h2>\n<p>Un syndrome qui se caract\u00e9rise par des sympt\u00f4mes invalidants. Notamment un raidissement des muscles du tronc et de l\u2019abdomen, suivi d\u2019une hypertrophie progressive. Une atteinte qui concerne \u00e9galement la musculature des bras et des jambes. L\u2019\u00e9volution, qui se d\u00e9roule sur des mois ou des ann\u00e9es, concerne peu \u00e0 peu tout le corps, avec la possibilit\u00e9 d\u2019une incapacit\u00e9 totale de se mouvoir. Des sympt\u00f4mes qui s\u2019accompagnent aussi d\u2019une sensibilit\u00e9 au bruit, au toucher, qui peut mener \u00e0 des crises de spasmes musculaires et \u00e0 des chutes.<br \/>\nCes sympt\u00f4mes constat\u00e9s aident \u00e0 poser le diagnostic, confirm\u00e9 par une \u00e9lectromyographie et des prises de sang. Ces analyses permettent aux m\u00e9decins de d\u00e9tecter l\u2019anticorps (anti-acide glutamique d\u00e9carboxylase) que l\u2019on retrouve fr\u00e9quemment chez les personnes atteintes par le syndrome de la personne raide.<br \/>\nLe diagnostic reste tr\u00e8s complexe \u00e0 \u00e9tablir. Le SPR est parfois confondu avec la maladie de Parkinson ou la <a href=\"https:\/\/www.fiftyandmemagazine.be\/fr\/bien-etre\/le-point-sur-une-maladie-meconnue-la-sclerose-en-plaques\" target=\"_blank\" rel=\"noopener\">scl\u00e9rose en plaques<\/a>. Dans certains cas, un scanner de la moelle \u00e9pini\u00e8re est recommand\u00e9 pour \u00e9liminer certaines causes m\u00e9caniques possibles (comme une hernie discale).<\/p>\n<h2>\nQuels traitements apporter ?<\/h2>\n<p>Les traitements apport\u00e9s ne visent pas \u00e0 gu\u00e9rir mais plut\u00f4t \u00e0 soulager la personne avec une action destin\u00e9e \u00e0 rel\u00e2cher les muscles. Comme le souligne le site <a href=\"http:\/\/www.orpha.net\" target=\"_blank\" rel=\"noopener\">Orphanet<\/a>, le portail d\u00e9di\u00e9 aux maladies rares, \u00ab plusieurs solutions sont g\u00e9n\u00e9ralement prises en compte par les m\u00e9decins. Dont l\u2019usage de benzodiaz\u00e9pines et de baclof\u00e8ne pour contrer la rigidit\u00e9 musculaire. Pour garder sous contr\u00f4le les sympt\u00f4mes, des th\u00e9rapies immuno-modulatrices, sous la forme de cortico\u00efdes ou d\u2019immunoglobulines intraveineuses, sont envisag\u00e9es \u00e9galement. \u00bb<\/p>\n<p>&nbsp;<\/p>\n<p><em>L\u2019article ne constitue nullement un avis m\u00e9dical et ne refl\u00e8te pas la situation m\u00e9dicale de la star.<\/em><\/p>\n<p><em>Photo Shutterstock.<\/em><\/p>\n","protected":false},"excerpt":{"rendered":"<p><span class=\"span-reading-time rt-reading-time\" style=\"display: block;\"><span class=\"rt-label rt-prefix\">Reading Time: <\/span> <span class=\"rt-time\"> 2<\/span> <span class=\"rt-label rt-postfix\">minutes<\/span><\/span>Les fans de C\u00e9line Dion ont appris le report en [&hellip;]<\/p>\n","protected":false},"author":11,"featured_media":56868,"comment_status":"open","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"","_lmt_disable":"","footnotes":""},"categories":[1065],"tags":[],"class_list":["post-56867","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-sante"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>C\u00e9line Dion : en quoi consiste sa maladie ? - Fifty &amp; Me MAGAZINE<\/title>\n<meta name=\"description\" content=\"C\u00e9line Dion a annonc\u00e9 souffrir du syndrome de la personne raide. 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